BOLA3 Antibody

Datasheet

Code	CSB-PA690486LA01HU
Size	US$166
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Image	Immunohistochemistry of paraffin-embedded human kidney tissue using CSB-PA690486LA01HU at dilution of 1:100
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Product Details
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Target Background

Product Details

Full Product Name

Rabbit anti-Homo sapiens (Human) BOLA3 Polyclonal antibody

Uniprot No.

Q53S33

Target Names

BOLA3

Alternative Names

BolA-like protein 3 antibody; BOLA3 antibody; BOLA3_HUMAN antibody; MMDS2 antibody

Raised in

Rabbit

Species Reactivity

Human

Immunogen

Recombinant Human BolA-like protein 3 protein (1-79AA)

Immunogen Species

Homo sapiens (Human)

Conjugate

Non-conjugated

The BOLA3 Antibody (Product code: CSB-PA690486LA01HU) is Non-conjugated. For BOLA3 Antibody with conjugates, please check the following table.

Conjugate	Product Code	Product Name	Application
HRP	CSB-PA690486LB01HU	BOLA3 Antibody, HRP conjugated	ELISA
FITC	CSB-PA690486LC01HU	BOLA3 Antibody, FITC conjugated
Biotin	CSB-PA690486LD01HU	BOLA3 Antibody, Biotin conjugated	ELISA

Clonality

Polyclonal

Isotype

IgG

Purification Method

>95%, Protein G purified

Concentration

It differs from different batches. Please contact us to confirm it.

Buffer

Preservative: 0.03% Proclin 300
Constituents: 50% Glycerol, 0.01M PBS, PH 7.4

Form

Liquid

Tested Applications

ELISA, IHC

Recommended Dilution

Application	Recommended Dilution
IHC	1:20-1:200

Protocols

ELISA Protocol
Immunohistochemistry (IHC) Protocol

Troubleshooting and FAQs

Antibody FAQs

Storage

Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.

Lead Time

Basically, we can dispatch the products out in 1-3 working days after receiving your orders. Delivery time maybe differs from different purchasing way or location, please kindly consult your local distributors for specific delivery time.

Usage

For Research Use Only. Not for use in diagnostic or therapeutic procedures.

Customer Reviews and Q&A

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Target Background

Function

Acts as a mitochondrial iron-sulfur (Fe-S) cluster assembly factor that facilitates (Fe-S) cluster insertion into a subset of mitochondrial proteins. Probably acts together with NFU1.

Gene References into Functions

Clinical features of BOLA3-associated variant nonketotic hyperglycemia include severe neurodegeneration after a period of normal development. PMID: 24334290
BOLA3 plays a crucial role in the biogenesis of iron-sulfur clusters. PMID: 22562699
Mutations in iron-sulfur cluster scaffold genes NFU1 and BOLA3 cause a fatal deficiency of multiple respiratory chain and 2-oxoacid dehydrogenase enzymes [case report] PMID: 21944046
Clinical trial of gene-disease association and gene-environment interaction. (HuGE Navigator) PMID: 20379614
This study reported that all three human BolA proteins (hBolA1, hBolA2, and hBolA3) are novel non-classical secreted proteins identified with bioinformatics and molecular biology experiments. PMID: 18548201
BOLA-like proteins are widely conserved from prokaryotes to eukaryotes and may be involved in cell proliferation or cell-cycle regulation. PMID: 14718656

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Involvement in disease

Multiple mitochondrial dysfunctions syndrome 2 with hyperglycinemia (MMDS2)

Subcellular Location

Mitochondrion.

Protein Families

BolA/IbaG family

Tissue Specificity

Widely expressed.

Database Links

HGNC: 24415

OMIM: 613183

KEGG: hsa:388962

STRING: 9606.ENSP00000331369

UniGene: Hs.61472

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Email: [email protected]
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Service

Phage Display Service

Antibody Service

Protein Service

Gene Synthesis Service

Oligo Synthesis Service

Antibody FAQs What Is an Antibody? How to Choose an Antibody for Scientific Research? The difference between primary antibody and secondary antibod The Meaning of Irregular Antibody Screening Tag Antibodies, Your Good Partner in Protein Research How to Choose the Loading Control Antibodies?

Call us

301-363-4651 (Available 9 a.m. to 5 p.m. CST from Monday to Friday)

[email protected]

Address

7505 Fannin St., Ste 610, Room 7 (CUBIO Innovation Center), Houston, TX 77054, USA

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