ASL (Argininosuccinate Lyase) is a protein coding gene that encodes a member of the lyase 1 family. The encoded protein forms a cytosolic homotetramer and primarily catalyzes the reversible hydrolytic cleavage of argininosuccinate into arginine and fumarate, an essential step in the liver in detoxifying ammonia via the urea cycle. Mutations in this gene result in the autosomal recessive disorder argininosuccinic aciduria, or argininosuccinic acid lyase deficiency. Diseases associated with ASL include Argininosuccinic Aciduria and Urea Cycle Disorder. Among its related pathways are Arginine biosynthesis and Viral mRNA Translation.
The following ASL reagents supplied by CUSABIO are manufactured under a strict quality control system. Multiple applications have been validated and solid technical support is offered.
ASL Antibodies for Homo sapiens (Human)
Code | Product Name | Species Reactivity | Application |
---|---|---|---|
CSB-PA883226 | ASL Antibody |
Human,Mouse,Rat | ELISA,IHC |
CSB-PA002213LA01HU | ASL Antibody |
Human | ELISA, IHC, IF |
ASL Proteins for Rattus norvegicus (Rat)
Code | Product Name | Source |
---|---|---|
CSB-YP002213RA CSB-EP002213RA CSB-BP002213RA CSB-MP002213RA CSB-EP002213RA-B |
Recombinant Rat Argininosuccinate lyase (Asl) |
Yeast E.coli Baculovirus Mammalian cell In Vivo Biotinylation in E.coli |
ASL Proteins for Homo sapiens (Human)
Code | Product Name | Source |
---|---|---|
CSB-YP002213HU CSB-EP002213HU CSB-BP002213HU CSB-MP002213HU CSB-EP002213HU-B |
Recombinant Human Argininosuccinate lyase (ASL) |
Yeast E.coli Baculovirus Mammalian cell In Vivo Biotinylation in E.coli |
ASL Proteins for Anser anser anser (Western greylag goose)
Code | Product Name | Source |
---|---|---|
CSB-YP002213AKX CSB-EP002213AKX CSB-BP002213AKX CSB-MP002213AKX CSB-EP002213AKX-B |
Recombinant Anser anser anser Argininosuccinate lyase (ASL) |
Yeast E.coli Baculovirus Mammalian cell In Vivo Biotinylation in E.coli |
ASL Proteins for Lithobates catesbeiana (American bullfrog) (Rana catesbeiana)
Code | Product Name | Source |
---|---|---|
CSB-YP002213LQA CSB-EP002213LQA CSB-BP002213LQA CSB-MP002213LQA CSB-EP002213LQA-B |
Recombinant Lithobates catesbeiana Argininosuccinate lyase (ASL) |
Yeast E.coli Baculovirus Mammalian cell In Vivo Biotinylation in E.coli |
ASL Proteins for Macaca fascicularis (Crab-eating macaque) (Cynomolgus monkey)
Code | Product Name | Source |
---|---|---|
CSB-YP002213MOV CSB-EP002213MOV CSB-BP002213MOV CSB-MP002213MOV CSB-EP002213MOV-B |
Recombinant Macaca fascicularis Argininosuccinate lyase (ASL) |
Yeast E.coli Baculovirus Mammalian cell In Vivo Biotinylation in E.coli |
ASL Proteins for Mus musculus (Mouse)
Code | Product Name | Source |
---|---|---|
CSB-YP002213MO CSB-EP002213MO CSB-BP002213MO CSB-MP002213MO CSB-EP002213MO-B |
Recombinant Mouse Argininosuccinate lyase (Asl) |
Yeast E.coli Baculovirus Mammalian cell In Vivo Biotinylation in E.coli |
ASL Proteins for Bos taurus (Bovine)
Code | Product Name | Source |
---|---|---|
CSB-YP002213BO CSB-EP002213BO CSB-BP002213BO CSB-MP002213BO CSB-EP002213BO-B |
Recombinant Bovine Argininosuccinate lyase (ASL) |
Yeast E.coli Baculovirus Mammalian cell In Vivo Biotinylation in E.coli |