SARDH, full name succinic semialdehyde dehydrogenase, also known as SSADH. It is a mitochondrial metabolic enzyme involved in γ-aminobutyric acid metabolism, maintaining GABA homeostasis and regulating nervous system function. SARDH deficiency causes GABA metabolic disorders, leading to hereditary neurometabolic diseases. Its dysregulation also correlates with liver diseases and cancers. SARDH enzyme replacement therapies are under preclinical research.
The following SARDH reagents supplied by CUSABIO are manufactured under a strict quality control system. Multiple applications have been validated and solid technical support is offered.
SARDH Proteins for Homo sapiens (Human)
| Code | Product Name | Source |
|---|---|---|
| CSB-YP891956HU CSB-EP891956HU CSB-BP891956HU CSB-MP891956HU CSB-EP891956HU-B |
Recombinant Human Sarcosine dehydrogenase, mitochondrial (SARDH), partial | Yeast E.coli Baculovirus Mammalian cell In Vivo Biotinylation in E.coli |